Prion disease: Review of the literature.

Prion disease are entities of unknown genetic origin that cause in human beings a number of neurological manifestations that lead patients to states of immobility and severe deterioration, with a very poor prognosis and uncertain cure rates. It is difficult to find in the literature important findin...

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Autores:
Tipo de recurso:
Fecha de publicación:
2022
Institución:
Pontificia Universidad Javeriana Cali
Repositorio:
Vitela
Idioma:
spa
OAI Identifier:
oai:vitela.javerianacali.edu.co:11522/495
Acceso en línea:
https://revistas.javerianacali.edu.co/index.php/salutemscientiaspiritus/article/view/695
https://vitela.javerianacali.edu.co/handle/11522/495
Palabra clave:
Deterioro neurológico
Priones
Manifestaciones clínicas
Encefalitis
Neurological deterioration
Prions
Clinical manifestations
Encephalitis
Rights
License
Derechos de autor 2023 Salutem Scientia Spiritus
id Vitela2_cdf874aeb89738f2530e3776e6edede0
oai_identifier_str oai:vitela.javerianacali.edu.co:11522/495
network_acronym_str Vitela2
network_name_str Vitela
repository_id_str
spelling Hernández, JonattanZaninovich-Ruiz, MilizaValencia, Henry2022-04-302023-10-11T04:35:10Z2023-10-11T04:35:10Zhttps://revistas.javerianacali.edu.co/index.php/salutemscientiaspiritus/article/view/695https://vitela.javerianacali.edu.co/handle/11522/495Prion disease are entities of unknown genetic origin that cause in human beings a number of neurological manifestations that lead patients to states of immobility and severe deterioration, with a very poor prognosis and uncertain cure rates. It is difficult to find in the literature important findings to determine the clinical diagnosis and pharmacological methodology to counteract the deterioration of patients suffering from this condition. Therefore, a systematic search was carried out in the PubMed database. Research from 1990 to 2020 that addressed the diagnostic criteria of Creutzfeldt-Jackobs disease in adults, its clinical manifestations, diagnosis and management, recommendations and management guidelines were included to demonstrate the situation of patients who present this type of alterations and deterioration neurological diagnosis of difficult diagnosis, to determine clinical criteria that can give a clinical orientation for the diagnosis of these entities.La enfermedad por priones, son entidades de origen genético desconocido que ocasiona en los seres humano un sin número de manifestaciones neurológicas que llevan a los pacientes a estados de inmovilidad y deterioro severo, con muy mal pronóstico y con tasas curativas inciertas. Es difícil encontrar en la literatura hallazgos importantes para determinar el diagnóstico clínico y metodología farmacológica para contrarrestar el deterioro de los pacientes que sufren dicha afección. Por lo anterior Se realizó una búsqueda sistemática en la base de datos PubMed. Se incluyeron investigaciones desde 1990 hasta 2020 que abordaran los criterios diagnósticos de la enfermedad por Creutzfeldt-Jackobs en adultos, sus manifestaciones clínicas, diagnóstico y manejo, recomendaciones y guías de manejo para evidenciar la situación de los pacientes quienes presentan este tipo de alteraciones y deterioro neurológico de difícil diagnóstico, para determinar criterios clínicos que puedan dar una orientación clínica para el diagnóstico de estas entidades.application/pdfspaPontificia Universidad Javeriana Calihttps://revistas.javerianacali.edu.co/index.php/salutemscientiaspiritus/article/view/695/591Derechos de autor 2023 Salutem Scientia Spiritushttps://creativecommons.org/licenses/by-nc-nd/4.0Salutem Scientia Spiritus; Vol. 8 No. 1 (2022): Revista Salutem Scientia Spiritus; 66-72Salutem Scientia Spiritus; Vol. 8 Núm. 1 (2022): Revista Salutem Scientia Spiritus; 66-722463-1426Deterioro neurológicoPrionesManifestaciones clínicasEncefalitisNeurological deteriorationPrionsClinical manifestationsEncephalitisPrion disease: Review of the literature.Enfermedad por priones: Revisión de la literatura.info:eu-repo/semantics/articleinfo:eu-repo/semantics/publishedVersionRevisión de la literatura11522/495oai:vitela.javerianacali.edu.co:11522/4952024-06-25 05:12:43.092metadata.onlyhttps://vitela.javerianacali.edu.coRepositorio Vitelavitela.mail@javerianacali.edu.co
dc.title.en-US.fl_str_mv Prion disease: Review of the literature.
dc.title.es-ES.fl_str_mv Enfermedad por priones: Revisión de la literatura.
title Prion disease: Review of the literature.
spellingShingle Prion disease: Review of the literature.
Hernández, Jonattan
Deterioro neurológico
Priones
Manifestaciones clínicas
Encefalitis
Neurological deterioration
Prions
Clinical manifestations
Encephalitis
title_short Prion disease: Review of the literature.
title_full Prion disease: Review of the literature.
title_fullStr Prion disease: Review of the literature.
title_full_unstemmed Prion disease: Review of the literature.
title_sort Prion disease: Review of the literature.
dc.creator.none.fl_str_mv Hernández, Jonattan
Zaninovich-Ruiz, Miliza
Valencia, Henry
author Hernández, Jonattan
author_facet Hernández, Jonattan
Zaninovich-Ruiz, Miliza
Valencia, Henry
author_role author
author2 Zaninovich-Ruiz, Miliza
Valencia, Henry
author2_role author
author
dc.subject.es-ES.fl_str_mv Deterioro neurológico
Priones
Manifestaciones clínicas
Encefalitis
topic Deterioro neurológico
Priones
Manifestaciones clínicas
Encefalitis
Neurological deterioration
Prions
Clinical manifestations
Encephalitis
dc.subject.en-US.fl_str_mv Neurological deterioration
Prions
Clinical manifestations
Encephalitis
description Prion disease are entities of unknown genetic origin that cause in human beings a number of neurological manifestations that lead patients to states of immobility and severe deterioration, with a very poor prognosis and uncertain cure rates. It is difficult to find in the literature important findings to determine the clinical diagnosis and pharmacological methodology to counteract the deterioration of patients suffering from this condition. Therefore, a systematic search was carried out in the PubMed database. Research from 1990 to 2020 that addressed the diagnostic criteria of Creutzfeldt-Jackobs disease in adults, its clinical manifestations, diagnosis and management, recommendations and management guidelines were included to demonstrate the situation of patients who present this type of alterations and deterioration neurological diagnosis of difficult diagnosis, to determine clinical criteria that can give a clinical orientation for the diagnosis of these entities.
publishDate 2022
dc.date.accessioned.none.fl_str_mv 2023-10-11T04:35:10Z
dc.date.available.none.fl_str_mv 2023-10-11T04:35:10Z
dc.date.none.fl_str_mv 2022-04-30
dc.type.none.fl_str_mv info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion
dc.type.es-ES.fl_str_mv Revisión de la literatura
status_str publishedVersion
dc.identifier.none.fl_str_mv https://revistas.javerianacali.edu.co/index.php/salutemscientiaspiritus/article/view/695
dc.identifier.uri.none.fl_str_mv https://vitela.javerianacali.edu.co/handle/11522/495
url https://revistas.javerianacali.edu.co/index.php/salutemscientiaspiritus/article/view/695
https://vitela.javerianacali.edu.co/handle/11522/495
dc.language.none.fl_str_mv spa
language spa
dc.relation.none.fl_str_mv https://revistas.javerianacali.edu.co/index.php/salutemscientiaspiritus/article/view/695/591
dc.rights.es-ES.fl_str_mv Derechos de autor 2023 Salutem Scientia Spiritus
https://creativecommons.org/licenses/by-nc-nd/4.0
rights_invalid_str_mv Derechos de autor 2023 Salutem Scientia Spiritus
https://creativecommons.org/licenses/by-nc-nd/4.0
dc.format.none.fl_str_mv application/pdf
dc.publisher.es-ES.fl_str_mv Pontificia Universidad Javeriana Cali
dc.source.en-US.fl_str_mv Salutem Scientia Spiritus; Vol. 8 No. 1 (2022): Revista Salutem Scientia Spiritus; 66-72
dc.source.es-ES.fl_str_mv Salutem Scientia Spiritus; Vol. 8 Núm. 1 (2022): Revista Salutem Scientia Spiritus; 66-72
dc.source.none.fl_str_mv 2463-1426
institution Pontificia Universidad Javeriana Cali
repository.name.fl_str_mv Repositorio Vitela
repository.mail.fl_str_mv vitela.mail@javerianacali.edu.co
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