Late-onset chorea after cerebral revascularization as a clinical manifestation of moyamoya disease

Moyamoya disease is a cerebral arteriopathy with an incidence of 0.086 per 100,000 inhabitants, being more common in women and Asian population. It has a broad spectrum of clinical manifestations including movement disorders, which can occur more frequently at clinical debut. The following is an unu...

Full description

Autores:
Enríquez Ruano, Pilar
Navarro, Cristian Eduardo
Penagos, Natalia
Espitia, Oscar Mauricio
Tipo de recurso:
Article of journal
Fecha de publicación:
2021
Institución:
Universidad El Bosque
Repositorio:
Repositorio U. El Bosque
Idioma:
eng
OAI Identifier:
oai:repositorio.unbosque.edu.co:20.500.12495/6714
Acceso en línea:
http://hdl.handle.net/20.500.12495/6714
https://doi.org/10.1007/s10072-021-05189-z
Palabra clave:
Enfermedad de Moyamoya
Arteriopatía cerebral
Encefaloduroarteriosinangiosis (EDAS)
Sintomatología motora
Arteria carótida interna
Arterias cerebrales
Moyamoya disease
Cerebral arteriopathy
Encephaloduroarteriosinangiosis (EDAS)
Motor symptomatology
Internal carotid artery
Cerebral arteries
Rights
openAccess
License
Acceso abierto
Description
Summary:Moyamoya disease is a cerebral arteriopathy with an incidence of 0.086 per 100,000 inhabitants, being more common in women and Asian population. It has a broad spectrum of clinical manifestations including movement disorders, which can occur more frequently at clinical debut. The following is an unusual case of late-onset chorea after cerebral revascularization, in medical literature only 3 cases like this have been described to our knowledge. A 4-year-old girl was admitted in 2015 for focal seizures, with an unremarkable physical examination. She had no relevant data in her past pre-/perinatal history and the neurological development was normal. Brain magnetic resonance imaging (MRI) was negative to lesions. The patient was treated with carbamazepine and levetiracetam, with satisfactory seizure control. Three years later, she had acute alternating hemiparesis, and cerebral arteriography showed decreased caliber of the left middle cerebral artery and multiple small vessels of perimesencephalic and basal ganglia location. Moyamoya disease was diagnosed at that moment. Thereafter, an encephaloduroarteriosynangiosis (EDAS) was carried out obtaining a full recovery of the motor symptoms.