A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy

Autores:: Kancherla, Vijaya
Tandaki, Lucita
Sundar, Manasvi
Lux, Anke
Bakker, Marian K.
Bergman, Jorieke EH.
Bermejo-Sánchez, Eva
Canfield, Mark A.
Feldkamp, Marcia L.
Groisman, Boris
Hurtado-Villa, Paula
Källén, Karin
Landau, Danielle
Lelong, Nathalie
Lopez-Camelo, Jorge
Mastroiacovo, Pierpaolo
Morgan, Margery
Mutchinick, Osvaldo M.
Nance, Amy E.
Nembhard, Wendy N.
Pierini, Anna
Šípek, Antonin
Stallings, Erin B.
Szabova, Elena
Wertelecki, Wladimir
Zarante, Ignacio
Rissmann, Anke

Tipo de recurso:: Article of journal

Fecha de publicación:: 2022

Institución:: Pontificia Universidad Javeriana

Repositorio:: Repositorio Universidad Javeriana

Idioma:: eng

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dc.title.spa.fl_str_mv	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy
title	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy
spellingShingle	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy Birth defects Bladder exstrophy Epidemiology Mortality Prevalence Surveillance
title_short	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy
title_full	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy
title_fullStr	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy
title_full_unstemmed	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy
title_sort	A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy
dc.creator.fl_str_mv	Kancherla, Vijaya Tandaki, Lucita Sundar, Manasvi Lux, Anke Bakker, Marian K. Bergman, Jorieke EH. Bermejo-Sánchez, Eva Canfield, Mark A. Feldkamp, Marcia L. Groisman, Boris Hurtado-Villa, Paula Källén, Karin Landau, Danielle Lelong, Nathalie Lopez-Camelo, Jorge Mastroiacovo, Pierpaolo Morgan, Margery Mutchinick, Osvaldo M. Nance, Amy E. Nembhard, Wendy N. Pierini, Anna Šípek, Antonin Stallings, Erin B. Szabova, Elena Wertelecki, Wladimir Zarante, Ignacio Rissmann, Anke
dc.contributor.author.none.fl_str_mv	Kancherla, Vijaya Tandaki, Lucita Sundar, Manasvi Lux, Anke Bakker, Marian K. Bergman, Jorieke EH. Bermejo-Sánchez, Eva Canfield, Mark A. Feldkamp, Marcia L. Groisman, Boris Hurtado-Villa, Paula Källén, Karin Landau, Danielle Lelong, Nathalie Lopez-Camelo, Jorge Mastroiacovo, Pierpaolo Morgan, Margery Mutchinick, Osvaldo M. Nance, Amy E. Nembhard, Wendy N. Pierini, Anna Šípek, Antonin Stallings, Erin B. Szabova, Elena Wertelecki, Wladimir Zarante, Ignacio Rissmann, Anke
dc.contributor.corporatename.spa.fl_str_mv	Pontificia Universidad Javeriana. Facultad de Medicina. Instituto de Genética Humana. Grupo de investigación Instituto de Genética Humana
dc.contributor.javerianateacher.none.fl_str_mv	Zarante, Ignacio
dc.subject.keyword.spa.fl_str_mv	Birth defects Bladder exstrophy Epidemiology Mortality Prevalence Surveillance
topic	Birth defects Bladder exstrophy Epidemiology Mortality Prevalence Surveillance
description	Q2
publishDate	2022
dc.date.accessioned.none.fl_str_mv	2022-10-20T12:59:07Z
dc.date.available.none.fl_str_mv	2022-10-20T12:59:07Z
dc.date.created.none.fl_str_mv	2022-05-29
dc.type.local.spa.fl_str_mv	Artículo de revista
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dc.identifier.issn.spa.fl_str_mv	0735-1631 / 1098-8785 (Electrónico)
dc.identifier.uri.none.fl_str_mv	http://hdl.handle.net/10554/62131
dc.identifier.doi.spa.fl_str_mv	https://doi.org/10.1055/s-0042-1748318
dc.identifier.instname.spa.fl_str_mv	instname:Pontificia Universidad Javeriana
dc.identifier.reponame.spa.fl_str_mv	reponame:Repositorio Institucional - Pontificia Universidad Javeriana
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identifier_str_mv	0735-1631 / 1098-8785 (Electrónico) instname:Pontificia Universidad Javeriana reponame:Repositorio Institucional - Pontificia Universidad Javeriana repourl:https://repository.javeriana.edu.co
dc.language.iso.spa.fl_str_mv	eng
language	eng
dc.relation.citationstartpage.spa.fl_str_mv	1
dc.relation.citationendpage.spa.fl_str_mv	12
dc.relation.ispartofjournal.spa.fl_str_mv	American Journal of Perinatology
dc.rights.licence.*.fl_str_mv	Atribución-NoComercial 4.0 Internacional
dc.rights.uri.*.fl_str_mv	http://creativecommons.org/licenses/by-nc/4.0/
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rights_invalid_str_mv	Atribución-NoComercial 4.0 Internacional http://creativecommons.org/licenses/by-nc/4.0/ http://purl.org/coar/access_right/c_abf2
dc.format.spa.fl_str_mv	PDF
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dc.coverage.temporal.none.fl_str_mv	2000-2014
institution	Pontificia Universidad Javeriana
bitstream.url.fl_str_mv	http://repository.javeriana.edu.co/bitstream/10554/62131/1/A%20Multicountry%20Analysis%20of%20Prevalence%20and%20Mortality%20among%20Neonates%20and%20Children%20with%20Bladder%20Exstrophy.pdf http://repository.javeriana.edu.co/bitstream/10554/62131/2/license.txt http://repository.javeriana.edu.co/bitstream/10554/62131/4/A%20Multicountry%20Analysis%20of%20Prevalence%20and%20Mortality%20among%20Neonates%20and%20Children%20with%20Bladder%20Exstrophy.pdf.jpg
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repository.name.fl_str_mv	Repositorio Institucional - Pontificia Universidad Javeriana
repository.mail.fl_str_mv	repositorio@javeriana.edu.co
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spelling	Atribución-NoComercial 4.0 Internacionalhttp://creativecommons.org/licenses/by-nc/4.0/http://purl.org/coar/access_right/c_abf2Kancherla, VijayaTandaki, LucitaSundar, ManasviLux, AnkeBakker, Marian K.Bergman, Jorieke EH.Bermejo-Sánchez, EvaCanfield, Mark A.Feldkamp, Marcia L.Groisman, BorisHurtado-Villa, PaulaKällén, KarinLandau, DanielleLelong, NathalieLopez-Camelo, JorgeMastroiacovo, PierpaoloMorgan, MargeryMutchinick, Osvaldo M.Nance, Amy E.Nembhard, Wendy N.Pierini, AnnaŠípek, AntoninStallings, Erin B.Szabova, ElenaWertelecki, WladimirZarante, IgnacioRissmann, AnkePontificia Universidad Javeriana. Facultad de Medicina. Instituto de Genética Humana. Grupo de investigación Instituto de Genética HumanaZarante, Ignacio2000-20142022-10-20T12:59:07Z2022-10-20T12:59:07Z2022-05-29https://login.ezproxy.javeriana.edu.co/login?qurl=https%3a%2f%2fsearch.ebscohost.com%2flogin.aspx%3fdirect%3dtrue%26AuthType%3dip%26db%3dmnh%26AN%3d35644130%26lang%3des%26site%3deds-live0735-1631 / 1098-8785 (Electrónico)http://hdl.handle.net/10554/62131https://doi.org/10.1055/s-0042-1748318instname:Pontificia Universidad Javerianareponame:Repositorio Institucional - Pontificia Universidad Javerianarepourl:https://repository.javeriana.edu.coPDFapplication/pdfengA Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder ExstrophyArtículo de revistahttp://purl.org/coar/resource_type/c_6501Q2Q1Recién nacidos y niñosObjective: Bladder exstrophy (BE) is a rare but severe birth defect affecting the lower abdominal wall and genitourinary system. The objective of the study is to examine the total prevalence, trends in prevalence, and age-specific mortality among individuals with BE. Study Design: We conducted a retrospective cohort study. Data were analyzed from 20 birth defects surveillance programs, members of the International Clearinghouse for Birth Defects Surveillance and Research in 16 countries. Live births, stillbirths, and elective terminations of pregnancy for fetal anomaly (ETOPFA) diagnosed with BE from 1974 to 2014. Pooled and program-specific prevalence of BE per 100,000 total births was calculated. The 95% confidence intervals (CI) for prevalence were estimated using Poisson approximation of binomial distribution. Time trends in prevalence of BE from 2000 to 2014 were examined using Poisson regression. Proportion of deaths among BE cases was calculated on the day of birth, day 2 to 6, day 7 to 27, day 28 to 364, 1 to 4 years, and ≥5 years. Mortality analysis was stratified by isolated, multiple, and syndromic case status. Results: The pooled total prevalence of BE was 2.58 per 100,000 total births (95% CI = 2.40, 2.78) for study years 1974 to 2014. Prevalence varied over time with a decreasing trend from 2000 to 2014. The first-week mortality proportion was 3.5, 17.3, and 14.6% among isolated, multiple, and syndromic BE cases, respectively. The majority of first-week mortality occurred on the first day of life among isolated, multiple, and syndromic BE cases. The proportion of first-week deaths was higher among cases reported from programs in Latin America where ETOPFA services were not available. Conclusions: Prevalence of BE varied by program and showed a decreasing trend from 2000 to –2014. Mortality is a concern among multiple and syndromic cases, and a high proportion of deaths among cases occurred during the first week of life. Key Points: Total prevalence of BE was 2.58 per 100,000 births. Prevalence decreased from 2000 to 2014. The first-week mortality was 9.3%.https://orcid.org/0000-0002-0729-6866Revista Internacional - IndexadaA1NoBirth defectsBladder exstrophyEpidemiologyMortalityPrevalenceSurveillance112American Journal of PerinatologyORIGINALA Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy.pdfA Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy.pdfArtículoapplication/pdf586639http://repository.javeriana.edu.co/bitstream/10554/62131/1/A%20Multicountry%20Analysis%20of%20Prevalence%20and%20Mortality%20among%20Neonates%20and%20Children%20with%20Bladder%20Exstrophy.pdfc3084415ab34fea87ec6886f28c21072MD51embargoed access\|\|\|9999-10-19LICENSElicense.txtlicense.txttext/plain; charset=utf-82603http://repository.javeriana.edu.co/bitstream/10554/62131/2/license.txt2070d280cc89439d983d9eee1b17df53MD52embargoed access\|\|\|9999-10-19THUMBNAILA Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy.pdf.jpgA Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy.pdf.jpgIM Thumbnailimage/jpeg10530http://repository.javeriana.edu.co/bitstream/10554/62131/4/A%20Multicountry%20Analysis%20of%20Prevalence%20and%20Mortality%20among%20Neonates%20and%20Children%20with%20Bladder%20Exstrophy.pdf.jpg9fd699ca58583c71876dd997cb5cd2ebMD54open access10554/62131oai:repository.javeriana.edu.co:10554/621312022-10-25 09:37:33.693Repositorio Institucional - Pontificia Universidad Javerianarepositorio@javeriana.edu.co

A Multicountry Analysis of Prevalence and Mortality among Neonates and Children with Bladder Exstrophy

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