Fatal Hemoptysis Secondary To Fibro-Inflammatory Igg4-Related Lung Disease: A Case Report

IgG4-related disease (IgGe-RD) is a fibro-inflammatory condition that affects nearly every organ; it was initially describe in the pancreas, by lesions with plasma cell infiltration with IgG4+. It presents a dense lymphoplasmocytic infiltrate, occasionally pseudotumoral, with fibrotic stroma with a storiform pattern and obliterative phlebitis, the lung representation was characterized in 2011, two thirds of the patients had increased IgG4 levels, there is a response to steroids in early stages of the disease.

• Autores: Fernández, Liliana; Munoz, CA; Amariles, JP; Sua, LF
• Tipo de recurso: http://purl.org/coar/resource_type/c_c94f
• Fecha de publicación: 2016
• Institución: Universidad ICESI
• Repositorio: Repositorio ICESI
• Idioma: eng
• OAI Identifier: oai:repository.icesi.edu.co:10906/81358
• Acceso en línea: http://nebulosa.icesi.edu.co:2143/Search.do?product=WOS&SID=3Dr7QVLgmeqIWKgWekv&search_mode=GeneralSearch&prID=7c60fd71-06c4-42fa-819b-5a3803c616aa; http://www.atsjournals.org/doi/abs/10.1164/ajrccm-conference.2016.193.1_MeetingAbstracts.A1630; http://hdl.handle.net/10906/81358
• Palabra clave: Ciencias socio biomédicas; Enfermedad pulmonar; Medical sciences; Ciencias socio biomédicas; Sistema respiratorio
• Rights: openAccess
• License: https://creativecommons.org/licenses/by-nc-nd/4.0/