Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.

Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, wit...

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Fecha de publicación:
2016
Institución:
Universidad del Rosario
Repositorio:
Repositorio EdocUR - U. Rosario
Idioma:
eng
OAI Identifier:
oai:repository.urosario.edu.co:10336/25961
Acceso en línea:
https://doi.org/10.1016/j.jdcr.2015.10.009
https://repository.urosario.edu.co/handle/10336/25961
Palabra clave:
Myofibroblastic tumor
Paraneoplastic syndromes
Pemphigus vulgaris
Pediatrics
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spelling 2ffc19f6-71f1-4365-ab99-3e2c7802dd81-19eb18372-a866-439e-9bfb-feb278ce51d7-1ebe14399-ae73-44c5-b282-9f728bf63623-15cf7b0a2-f14f-41fa-ac2e-f0213ec41a89-1f128ead7-8a8e-4c04-9655-53a69f49cb04-1c39a1678-8b3a-4d2a-81c8-6a9f8827c6e5-14654f24c-c7af-4c79-8be9-d70830882236-14b1fe22d-8842-44fb-9bee-5428cf5ed5d5-1bc54c6d9-1d83-4a01-a34d-fa07bbdd2a4b-12020-08-06T16:20:19Z2020-08-06T16:20:19Z2016-01-26Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, with significant morbidity and mortality. This condition is clinically characterized by severe mucositis and polymorphic blistering skin eruptions, and histologically by acantholysis, keratinocyte necrosis, and interface dermatitis.3 Immunoprecipitation and immunoblot testing detect autoantibodies against desmosomal polypeptides.4 We describe a case of paraneoplastic pemphigus associated with an abdominal inflammatory myofibroblastic tumor in a 7-year-old girl.application/pdfhttps://doi.org/10.1016/j.jdcr.2015.10.009ISSN: 2352-5126https://repository.urosario.edu.co/handle/10336/25961engElsevier40No. 137JAAD case reportsVol. 2JAAD case reports, ISSN: 2352-5126, Vol.2, No.1 (January, 2016); pp.37-40https://www.jaadcasereports.org/article/S2352-5126(15)00174-5/fulltextAbierto (Texto Completo)http://purl.org/coar/access_right/c_abf2JAAD case reportsinstname:Universidad del Rosarioreponame:Repositorio Institucional EdocURMyofibroblastic tumorParaneoplastic syndromesPemphigus vulgarisPediatricsInflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.Tumor miofibroblástico inflamatorio que se presenta como pénfigo paraneoplásico en una niña de 7 años.articleArtículohttp://purl.org/coar/version/c_970fb48d4fbd8a85http://purl.org/coar/resource_type/c_6501Halpert, EvelyneFigueroa, Juan LuisRojas, ArmandoOrtiz, Clara InesChaparro, DanielaGalindo, MarcelaLammoglia, Juan JavierRumie, CarolinaOlmos, CarlosORIGINALPIIS2352512615001745.pdfapplication/pdf913376https://repository.urosario.edu.co/bitstreams/8db6ab61-326d-4230-b710-cdc3b3169b55/download7e9bb25f673cc121d192ce3136635e67MD51TEXTPIIS2352512615001745.pdf.txtPIIS2352512615001745.pdf.txtExtracted texttext/plain12394https://repository.urosario.edu.co/bitstreams/c68a00d0-d39a-4968-9a4f-751980775ab6/download9b5964ac16d084ac855aa74dfc411608MD52THUMBNAILPIIS2352512615001745.pdf.jpgPIIS2352512615001745.pdf.jpgGenerated Thumbnailimage/jpeg4701https://repository.urosario.edu.co/bitstreams/7cc83085-e24d-4eb8-bef8-8c9722925c8f/download3849750bde2019167e143e74f4cfd84eMD5310336/25961oai:repository.urosario.edu.co:10336/259612021-06-03 00:50:22.418https://repository.urosario.edu.coRepositorio institucional EdocURedocur@urosario.edu.co
dc.title.spa.fl_str_mv Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
dc.title.TranslatedTitle.spa.fl_str_mv Tumor miofibroblástico inflamatorio que se presenta como pénfigo paraneoplásico en una niña de 7 años.
title Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
spellingShingle Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
Myofibroblastic tumor
Paraneoplastic syndromes
Pemphigus vulgaris
Pediatrics
title_short Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
title_full Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
title_fullStr Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
title_full_unstemmed Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
title_sort Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
dc.subject.keyword.spa.fl_str_mv Myofibroblastic tumor
Paraneoplastic syndromes
Pemphigus vulgaris
Pediatrics
topic Myofibroblastic tumor
Paraneoplastic syndromes
Pemphigus vulgaris
Pediatrics
description Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, with significant morbidity and mortality. This condition is clinically characterized by severe mucositis and polymorphic blistering skin eruptions, and histologically by acantholysis, keratinocyte necrosis, and interface dermatitis.3 Immunoprecipitation and immunoblot testing detect autoantibodies against desmosomal polypeptides.4 We describe a case of paraneoplastic pemphigus associated with an abdominal inflammatory myofibroblastic tumor in a 7-year-old girl.
publishDate 2016
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dc.identifier.issn.none.fl_str_mv ISSN: 2352-5126
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https://repository.urosario.edu.co/handle/10336/25961
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dc.relation.citationTitle.none.fl_str_mv JAAD case reports
dc.relation.citationVolume.none.fl_str_mv Vol. 2
dc.relation.ispartof.spa.fl_str_mv JAAD case reports, ISSN: 2352-5126, Vol.2, No.1 (January, 2016); pp.37-40
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