Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.
Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, wit...
- Autores:
- Tipo de recurso:
- Fecha de publicación:
- 2016
- Institución:
- Universidad del Rosario
- Repositorio:
- Repositorio EdocUR - U. Rosario
- Idioma:
- eng
- OAI Identifier:
- oai:repository.urosario.edu.co:10336/25961
- Acceso en línea:
- https://doi.org/10.1016/j.jdcr.2015.10.009
https://repository.urosario.edu.co/handle/10336/25961
- Palabra clave:
- Myofibroblastic tumor
Paraneoplastic syndromes
Pemphigus vulgaris
Pediatrics
- Rights
- License
- Abierto (Texto Completo)
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2ffc19f6-71f1-4365-ab99-3e2c7802dd81-19eb18372-a866-439e-9bfb-feb278ce51d7-1ebe14399-ae73-44c5-b282-9f728bf63623-15cf7b0a2-f14f-41fa-ac2e-f0213ec41a89-1f128ead7-8a8e-4c04-9655-53a69f49cb04-1c39a1678-8b3a-4d2a-81c8-6a9f8827c6e5-14654f24c-c7af-4c79-8be9-d70830882236-14b1fe22d-8842-44fb-9bee-5428cf5ed5d5-1bc54c6d9-1d83-4a01-a34d-fa07bbdd2a4b-12020-08-06T16:20:19Z2020-08-06T16:20:19Z2016-01-26Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, with significant morbidity and mortality. This condition is clinically characterized by severe mucositis and polymorphic blistering skin eruptions, and histologically by acantholysis, keratinocyte necrosis, and interface dermatitis.3 Immunoprecipitation and immunoblot testing detect autoantibodies against desmosomal polypeptides.4 We describe a case of paraneoplastic pemphigus associated with an abdominal inflammatory myofibroblastic tumor in a 7-year-old girl.application/pdfhttps://doi.org/10.1016/j.jdcr.2015.10.009ISSN: 2352-5126https://repository.urosario.edu.co/handle/10336/25961engElsevier40No. 137JAAD case reportsVol. 2JAAD case reports, ISSN: 2352-5126, Vol.2, No.1 (January, 2016); pp.37-40https://www.jaadcasereports.org/article/S2352-5126(15)00174-5/fulltextAbierto (Texto Completo)http://purl.org/coar/access_right/c_abf2JAAD case reportsinstname:Universidad del Rosarioreponame:Repositorio Institucional EdocURMyofibroblastic tumorParaneoplastic syndromesPemphigus vulgarisPediatricsInflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl.Tumor miofibroblástico inflamatorio que se presenta como pénfigo paraneoplásico en una niña de 7 años.articleArtículohttp://purl.org/coar/version/c_970fb48d4fbd8a85http://purl.org/coar/resource_type/c_6501Halpert, EvelyneFigueroa, Juan LuisRojas, ArmandoOrtiz, Clara InesChaparro, DanielaGalindo, MarcelaLammoglia, Juan JavierRumie, CarolinaOlmos, CarlosORIGINALPIIS2352512615001745.pdfapplication/pdf913376https://repository.urosario.edu.co/bitstreams/8db6ab61-326d-4230-b710-cdc3b3169b55/download7e9bb25f673cc121d192ce3136635e67MD51TEXTPIIS2352512615001745.pdf.txtPIIS2352512615001745.pdf.txtExtracted texttext/plain12394https://repository.urosario.edu.co/bitstreams/c68a00d0-d39a-4968-9a4f-751980775ab6/download9b5964ac16d084ac855aa74dfc411608MD52THUMBNAILPIIS2352512615001745.pdf.jpgPIIS2352512615001745.pdf.jpgGenerated Thumbnailimage/jpeg4701https://repository.urosario.edu.co/bitstreams/7cc83085-e24d-4eb8-bef8-8c9722925c8f/download3849750bde2019167e143e74f4cfd84eMD5310336/25961oai:repository.urosario.edu.co:10336/259612021-06-03 00:50:22.418https://repository.urosario.edu.coRepositorio institucional EdocURedocur@urosario.edu.co |
dc.title.spa.fl_str_mv |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. |
dc.title.TranslatedTitle.spa.fl_str_mv |
Tumor miofibroblástico inflamatorio que se presenta como pénfigo paraneoplásico en una niña de 7 años. |
title |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. |
spellingShingle |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. Myofibroblastic tumor Paraneoplastic syndromes Pemphigus vulgaris Pediatrics |
title_short |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. |
title_full |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. |
title_fullStr |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. |
title_full_unstemmed |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. |
title_sort |
Inflammatory myofibroblastic tumor presenting as paraneoplastic pemphigus in a 7-year-old girl. |
dc.subject.keyword.spa.fl_str_mv |
Myofibroblastic tumor Paraneoplastic syndromes Pemphigus vulgaris Pediatrics |
topic |
Myofibroblastic tumor Paraneoplastic syndromes Pemphigus vulgaris Pediatrics |
description |
Paraneoplastic pemphigus is an autoimmune disease associated with an underlying tumor. Several cases have been reported as unusual pemphigus vulgaris, erythema multiforme, or paraneoplastic bullous disease,1 but the incidence of the condition is unknown.2 Response to treatment is generally poor, with significant morbidity and mortality. This condition is clinically characterized by severe mucositis and polymorphic blistering skin eruptions, and histologically by acantholysis, keratinocyte necrosis, and interface dermatitis.3 Immunoprecipitation and immunoblot testing detect autoantibodies against desmosomal polypeptides.4 We describe a case of paraneoplastic pemphigus associated with an abdominal inflammatory myofibroblastic tumor in a 7-year-old girl. |
publishDate |
2016 |
dc.date.created.spa.fl_str_mv |
2016-01-26 |
dc.date.accessioned.none.fl_str_mv |
2020-08-06T16:20:19Z |
dc.date.available.none.fl_str_mv |
2020-08-06T16:20:19Z |
dc.type.eng.fl_str_mv |
article |
dc.type.coarversion.fl_str_mv |
http://purl.org/coar/version/c_970fb48d4fbd8a85 |
dc.type.coar.fl_str_mv |
http://purl.org/coar/resource_type/c_6501 |
dc.type.spa.spa.fl_str_mv |
Artículo |
dc.identifier.doi.none.fl_str_mv |
https://doi.org/10.1016/j.jdcr.2015.10.009 |
dc.identifier.issn.none.fl_str_mv |
ISSN: 2352-5126 |
dc.identifier.uri.none.fl_str_mv |
https://repository.urosario.edu.co/handle/10336/25961 |
url |
https://doi.org/10.1016/j.jdcr.2015.10.009 https://repository.urosario.edu.co/handle/10336/25961 |
identifier_str_mv |
ISSN: 2352-5126 |
dc.language.iso.spa.fl_str_mv |
eng |
language |
eng |
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40 |
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No. 1 |
dc.relation.citationStartPage.none.fl_str_mv |
37 |
dc.relation.citationTitle.none.fl_str_mv |
JAAD case reports |
dc.relation.citationVolume.none.fl_str_mv |
Vol. 2 |
dc.relation.ispartof.spa.fl_str_mv |
JAAD case reports, ISSN: 2352-5126, Vol.2, No.1 (January, 2016); pp.37-40 |
dc.relation.uri.spa.fl_str_mv |
https://www.jaadcasereports.org/article/S2352-5126(15)00174-5/fulltext |
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http://purl.org/coar/access_right/c_abf2 |
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Abierto (Texto Completo) |
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Abierto (Texto Completo) http://purl.org/coar/access_right/c_abf2 |
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application/pdf |
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Elsevier |
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JAAD case reports |
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Universidad del Rosario |
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reponame:Repositorio Institucional EdocUR |
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