Development of hip dysplasia in hereditary multiple exostosis

In approximately 25% of patients with hereditary multiple exostosis, there is an abnormal osteochondral formation localized in the femoral proximal metaphysis. This formation often causes a mechanically progressive insufficiency of the acetabular cavity, a true developmental hip dysplasia, that toge...

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Autores:
Tipo de recurso:
Fecha de publicación:
2001
Institución:
Universidad del Rosario
Repositorio:
Repositorio EdocUR - U. Rosario
Idioma:
eng
OAI Identifier:
oai:repository.urosario.edu.co:10336/22420
Acceso en línea:
https://doi.org/10.1097/01241398-200103000-00014
https://repository.urosario.edu.co/handle/10336/22420
Palabra clave:
Article
Cancer surgery
Child
Chondroma
Clinical article
Female
Genetic counseling
Hereditary multiple exostosis
Hip disease
Hip dysplasia
Human
Hyperostosis
Male
Osteochondroma
Priority journal
Coxa valga
Developmental dysplasia
Ext gene family
Femur-hip osteochondroma
Hereditary multiple exostosis
Hip
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Abierto (Texto Completo)
id EDOCUR2_9016e986f8ad0a60285e88961d2e479a
oai_identifier_str oai:repository.urosario.edu.co:10336/22420
network_acronym_str EDOCUR2
network_name_str Repositorio EdocUR - U. Rosario
repository_id_str
spelling 5cefaa73-bf47-459e-8329-b62bb42af834-12020-05-25T23:56:25Z2020-05-25T23:56:25Z2001In approximately 25% of patients with hereditary multiple exostosis, there is an abnormal osteochondral formation localized in the femoral proximal metaphysis. This formation often causes a mechanically progressive insufficiency of the acetabular cavity, a true developmental hip dysplasia, that together with a coxa valga deformity, which is also present, causes a gradual deterioration in the relations of this joint. This malformation has a poor prognosis and is difficult to manage. Although this entity is rather frequent and quite severe, it is rarely found in the medical literature. The author describes six private cases, taken from a total of 24,000 patients (0.25/1000) as examples of this entity, and provides a review of the literature.application/pdfhttps://doi.org/10.1097/01241398-200103000-000141539257002716798https://repository.urosario.edu.co/handle/10336/22420engLippincott Williams and Wilkins211No. 2205Journal of Pediatric OrthopaedicsVol. 21Journal of Pediatric Orthopaedics, ISSN:15392570, 02716798, Vol.21, No.2 (2001); pp. 205-211https://www.scopus.com/inward/record.uri?eid=2-s2.0-0035119756&doi=10.1097%2f01241398-200103000-00014&partnerID=40&md5=9b54328135faede1ca1025beef0774fcAbierto (Texto Completo)http://purl.org/coar/access_right/c_abf2instname:Universidad del Rosarioreponame:Repositorio Institucional EdocURArticleCancer surgeryChildChondromaClinical articleFemaleGenetic counselingHereditary multiple exostosisHip diseaseHip dysplasiaHumanHyperostosisMaleOsteochondromaPriority journalCoxa valgaDevelopmental dysplasiaExt gene familyFemur-hip osteochondromaHereditary multiple exostosisHipDevelopment of hip dysplasia in hereditary multiple exostosisarticleArtículohttp://purl.org/coar/version/c_970fb48d4fbd8a85http://purl.org/coar/resource_type/c_6501Malagón V.10336/22420oai:repository.urosario.edu.co:10336/224202022-05-02 07:37:14.156038https://repository.urosario.edu.coRepositorio institucional EdocURedocur@urosario.edu.co
dc.title.spa.fl_str_mv Development of hip dysplasia in hereditary multiple exostosis
title Development of hip dysplasia in hereditary multiple exostosis
spellingShingle Development of hip dysplasia in hereditary multiple exostosis
Article
Cancer surgery
Child
Chondroma
Clinical article
Female
Genetic counseling
Hereditary multiple exostosis
Hip disease
Hip dysplasia
Human
Hyperostosis
Male
Osteochondroma
Priority journal
Coxa valga
Developmental dysplasia
Ext gene family
Femur-hip osteochondroma
Hereditary multiple exostosis
Hip
title_short Development of hip dysplasia in hereditary multiple exostosis
title_full Development of hip dysplasia in hereditary multiple exostosis
title_fullStr Development of hip dysplasia in hereditary multiple exostosis
title_full_unstemmed Development of hip dysplasia in hereditary multiple exostosis
title_sort Development of hip dysplasia in hereditary multiple exostosis
dc.subject.keyword.spa.fl_str_mv Article
Cancer surgery
Child
Chondroma
Clinical article
Female
Genetic counseling
Hereditary multiple exostosis
Hip disease
Hip dysplasia
Human
Hyperostosis
Male
Osteochondroma
Priority journal
Coxa valga
Developmental dysplasia
Ext gene family
Femur-hip osteochondroma
Hereditary multiple exostosis
Hip
topic Article
Cancer surgery
Child
Chondroma
Clinical article
Female
Genetic counseling
Hereditary multiple exostosis
Hip disease
Hip dysplasia
Human
Hyperostosis
Male
Osteochondroma
Priority journal
Coxa valga
Developmental dysplasia
Ext gene family
Femur-hip osteochondroma
Hereditary multiple exostosis
Hip
description In approximately 25% of patients with hereditary multiple exostosis, there is an abnormal osteochondral formation localized in the femoral proximal metaphysis. This formation often causes a mechanically progressive insufficiency of the acetabular cavity, a true developmental hip dysplasia, that together with a coxa valga deformity, which is also present, causes a gradual deterioration in the relations of this joint. This malformation has a poor prognosis and is difficult to manage. Although this entity is rather frequent and quite severe, it is rarely found in the medical literature. The author describes six private cases, taken from a total of 24,000 patients (0.25/1000) as examples of this entity, and provides a review of the literature.
publishDate 2001
dc.date.created.spa.fl_str_mv 2001
dc.date.accessioned.none.fl_str_mv 2020-05-25T23:56:25Z
dc.date.available.none.fl_str_mv 2020-05-25T23:56:25Z
dc.type.eng.fl_str_mv article
dc.type.coarversion.fl_str_mv http://purl.org/coar/version/c_970fb48d4fbd8a85
dc.type.coar.fl_str_mv http://purl.org/coar/resource_type/c_6501
dc.type.spa.spa.fl_str_mv Artículo
dc.identifier.doi.none.fl_str_mv https://doi.org/10.1097/01241398-200103000-00014
dc.identifier.issn.none.fl_str_mv 15392570
02716798
dc.identifier.uri.none.fl_str_mv https://repository.urosario.edu.co/handle/10336/22420
url https://doi.org/10.1097/01241398-200103000-00014
https://repository.urosario.edu.co/handle/10336/22420
identifier_str_mv 15392570
02716798
dc.language.iso.spa.fl_str_mv eng
language eng
dc.relation.citationEndPage.none.fl_str_mv 211
dc.relation.citationIssue.none.fl_str_mv No. 2
dc.relation.citationStartPage.none.fl_str_mv 205
dc.relation.citationTitle.none.fl_str_mv Journal of Pediatric Orthopaedics
dc.relation.citationVolume.none.fl_str_mv Vol. 21
dc.relation.ispartof.spa.fl_str_mv Journal of Pediatric Orthopaedics, ISSN:15392570, 02716798, Vol.21, No.2 (2001); pp. 205-211
dc.relation.uri.spa.fl_str_mv https://www.scopus.com/inward/record.uri?eid=2-s2.0-0035119756&doi=10.1097%2f01241398-200103000-00014&partnerID=40&md5=9b54328135faede1ca1025beef0774fc
dc.rights.coar.fl_str_mv http://purl.org/coar/access_right/c_abf2
dc.rights.acceso.spa.fl_str_mv Abierto (Texto Completo)
rights_invalid_str_mv Abierto (Texto Completo)
http://purl.org/coar/access_right/c_abf2
dc.format.mimetype.none.fl_str_mv application/pdf
dc.publisher.spa.fl_str_mv Lippincott Williams and Wilkins
institution Universidad del Rosario
dc.source.instname.spa.fl_str_mv instname:Universidad del Rosario
dc.source.reponame.spa.fl_str_mv reponame:Repositorio Institucional EdocUR
repository.name.fl_str_mv Repositorio institucional EdocUR
repository.mail.fl_str_mv edocur@urosario.edu.co
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