Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis

Renal involvement in systemic sclerosis (SSc) has a negative influence on prognosis. Cases of SSc sine scleroderma have been reported in which organ failure occurred but was not accompanied by cutaneous damage, which in some instances did develop later. We describe a patient who, after 6 months of s...

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Tipo de recurso:
Fecha de publicación:
1995
Institución:
Universidad del Rosario
Repositorio:
Repositorio EdocUR - U. Rosario
Idioma:
eng
OAI Identifier:
oai:repository.urosario.edu.co:10336/27012
Acceso en línea:
https://repository.urosario.edu.co/handle/10336/27012
Palabra clave:
Systemic sclerosis
Scleroderma
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id EDOCUR2_68aca034609e97197722091a05e78413
oai_identifier_str oai:repository.urosario.edu.co:10336/27012
network_acronym_str EDOCUR2
network_name_str Repositorio EdocUR - U. Rosario
repository_id_str
spelling 1947477860068c1c9ca-f632-4e13-a1b4-d1d4ea62f0a40bce08a2-0b2f-4be5-9998-e1560dd4416f84c44ffc-ba42-4182-aa52-1869ff241d91489e8797-6464-4a2a-8b88-401115581aee2020-08-19T14:40:45Z2020-08-19T14:40:45Z1995Renal involvement in systemic sclerosis (SSc) has a negative influence on prognosis. Cases of SSc sine scleroderma have been reported in which organ failure occurred but was not accompanied by cutaneous damage, which in some instances did develop later. We describe a patient who, after 6 months of symmetric polyarthritis, developed rapid progressive renal failure without skin changes. A diagnosis of scleroderma renal crisis, confirmed histologically, was made. Anti-RNAP III antibodies were positive. The patient developed typical scleroderma skin changes after renal failure. Despite treatment, SSc advanced to fatal endstage renal disease.application/pdfISSN: 0315-162XEISSN: 1499-2752https://repository.urosario.edu.co/handle/10336/27012engEurope PMC2168No. 3163Journal of RheumatologyVol. 22Journal of Rheumatology, ISSN: 0315-162X;EISSN: 1499-2752, Vol.22, No.3 (28 Febrero 1995); pp. 163-2168https://europepmc.org/article/med/7783082Bloqueado (Texto referencial)http://purl.org/coar/access_right/c_14cbJournal of Rheumatologyinstname:Universidad del Rosarioreponame:Repositorio Institucional EdocURSystemic sclerosisSclerodermaSystemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisisEsclerodermia sistémica sinusoidal: una presentación inusual en la crisis renal por esclerodermiaarticleArtículohttp://purl.org/coar/version/c_970fb48d4fbd8a85http://purl.org/coar/resource_type/c_6501Anaya, Juan-ManuelMolina, JFCabrera, GEHoffman, E.Espinosa, LR10336/27012oai:repository.urosario.edu.co:10336/270122021-08-10 17:14:04.247https://repository.urosario.edu.coRepositorio institucional EdocURedocur@urosario.edu.co
dc.title.spa.fl_str_mv Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
dc.title.TranslatedTitle.spa.fl_str_mv Esclerodermia sistémica sinusoidal: una presentación inusual en la crisis renal por esclerodermia
title Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
spellingShingle Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
Systemic sclerosis
Scleroderma
title_short Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
title_full Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
title_fullStr Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
title_full_unstemmed Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
title_sort Systemic sclerosis sine scleroderma: An unusual presentation in scleroderma renal crisis
dc.subject.keyword.spa.fl_str_mv Systemic sclerosis
Scleroderma
topic Systemic sclerosis
Scleroderma
description Renal involvement in systemic sclerosis (SSc) has a negative influence on prognosis. Cases of SSc sine scleroderma have been reported in which organ failure occurred but was not accompanied by cutaneous damage, which in some instances did develop later. We describe a patient who, after 6 months of symmetric polyarthritis, developed rapid progressive renal failure without skin changes. A diagnosis of scleroderma renal crisis, confirmed histologically, was made. Anti-RNAP III antibodies were positive. The patient developed typical scleroderma skin changes after renal failure. Despite treatment, SSc advanced to fatal endstage renal disease.
publishDate 1995
dc.date.created.spa.fl_str_mv 1995
dc.date.accessioned.none.fl_str_mv 2020-08-19T14:40:45Z
dc.date.available.none.fl_str_mv 2020-08-19T14:40:45Z
dc.type.eng.fl_str_mv article
dc.type.coarversion.fl_str_mv http://purl.org/coar/version/c_970fb48d4fbd8a85
dc.type.coar.fl_str_mv http://purl.org/coar/resource_type/c_6501
dc.type.spa.spa.fl_str_mv Artículo
dc.identifier.issn.none.fl_str_mv ISSN: 0315-162X
EISSN: 1499-2752
dc.identifier.uri.none.fl_str_mv https://repository.urosario.edu.co/handle/10336/27012
identifier_str_mv ISSN: 0315-162X
EISSN: 1499-2752
url https://repository.urosario.edu.co/handle/10336/27012
dc.language.iso.spa.fl_str_mv eng
language eng
dc.relation.citationEndPage.none.fl_str_mv 2168
dc.relation.citationIssue.none.fl_str_mv No. 3
dc.relation.citationStartPage.none.fl_str_mv 163
dc.relation.citationTitle.none.fl_str_mv Journal of Rheumatology
dc.relation.citationVolume.none.fl_str_mv Vol. 22
dc.relation.ispartof.spa.fl_str_mv Journal of Rheumatology, ISSN: 0315-162X;EISSN: 1499-2752, Vol.22, No.3 (28 Febrero 1995); pp. 163-2168
dc.relation.uri.spa.fl_str_mv https://europepmc.org/article/med/7783082
dc.rights.coar.fl_str_mv http://purl.org/coar/access_right/c_14cb
dc.rights.acceso.spa.fl_str_mv Bloqueado (Texto referencial)
rights_invalid_str_mv Bloqueado (Texto referencial)
http://purl.org/coar/access_right/c_14cb
dc.format.mimetype.none.fl_str_mv application/pdf
dc.publisher.spa.fl_str_mv Europe PMC
dc.source.spa.fl_str_mv Journal of Rheumatology
institution Universidad del Rosario
dc.source.instname.none.fl_str_mv instname:Universidad del Rosario
dc.source.reponame.none.fl_str_mv reponame:Repositorio Institucional EdocUR
repository.name.fl_str_mv Repositorio institucional EdocUR
repository.mail.fl_str_mv edocur@urosario.edu.co
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