Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas

En este trabajo se describen los hallazgos extrapulmonares detectados por imágenes diagnósticas, de una población colombiana con fibrosis quística, atendida en dos centros de salud de Bogotá, Colombia.

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Tipo de recurso:
Fecha de publicación:
2023
Institución:
Universidad del Rosario
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Repositorio EdocUR - U. Rosario
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spa
OAI Identifier:
oai:repository.urosario.edu.co:10336/40772
Acceso en línea:
https://doi.org/10.48713/10336_40772
https://repository.urosario.edu.co/handle/10336/40772
Palabra clave:
Fibrosis quística
Manifestaciones extrapulmonares
Cystic fibrosis
Extrapulmonary manifestations
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Attribution-NonCommercial-NoDerivatives 4.0 International
id EDOCUR2_5a2b8012dc1019d5d6925ed39fb5d42a
oai_identifier_str oai:repository.urosario.edu.co:10336/40772
network_acronym_str EDOCUR2
network_name_str Repositorio EdocUR - U. Rosario
repository_id_str
dc.title.none.fl_str_mv Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
dc.title.TranslatedTitle.none.fl_str_mv Prevalence of extrapulmonary findings in patients with cystic fibrosis: identification by diagnostic images
title Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
spellingShingle Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
Fibrosis quística
Manifestaciones extrapulmonares
Cystic fibrosis
Extrapulmonary manifestations
title_short Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
title_full Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
title_fullStr Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
title_full_unstemmed Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
title_sort Prevalencia de hallazgos extrapulmonares en pacientes con fibrosis quística: identificación por imágenes diagnósticas
dc.contributor.advisor.none.fl_str_mv Pérez Alvarado, María Carolina
Pedraza Flechas, Ana María
dc.subject.none.fl_str_mv Fibrosis quística
Manifestaciones extrapulmonares
topic Fibrosis quística
Manifestaciones extrapulmonares
Cystic fibrosis
Extrapulmonary manifestations
dc.subject.keyword.none.fl_str_mv Cystic fibrosis
Extrapulmonary manifestations
description En este trabajo se describen los hallazgos extrapulmonares detectados por imágenes diagnósticas, de una población colombiana con fibrosis quística, atendida en dos centros de salud de Bogotá, Colombia.
publishDate 2023
dc.date.accessioned.none.fl_str_mv 2023-08-25T20:59:03Z
dc.date.available.none.fl_str_mv 2023-08-25T20:59:03Z
dc.date.created.none.fl_str_mv 2023-06-20
dc.type.none.fl_str_mv bachelorThesis
dc.type.coar.fl_str_mv http://purl.org/coar/resource_type/c_7a1f
dc.type.document.none.fl_str_mv Trabajo de grado
dc.type.spa.none.fl_str_mv Trabajo de grado
dc.identifier.doi.none.fl_str_mv https://doi.org/10.48713/10336_40772
dc.identifier.uri.none.fl_str_mv https://repository.urosario.edu.co/handle/10336/40772
url https://doi.org/10.48713/10336_40772
https://repository.urosario.edu.co/handle/10336/40772
dc.language.iso.none.fl_str_mv spa
language spa
dc.rights.*.fl_str_mv Attribution-NonCommercial-NoDerivatives 4.0 International
dc.rights.coar.fl_str_mv http://purl.org/coar/access_right/c_abf2
dc.rights.acceso.none.fl_str_mv Abierto (Texto Completo)
dc.rights.uri.*.fl_str_mv http://creativecommons.org/licenses/by-nc-nd/4.0/
rights_invalid_str_mv Attribution-NonCommercial-NoDerivatives 4.0 International
Abierto (Texto Completo)
http://creativecommons.org/licenses/by-nc-nd/4.0/
http://purl.org/coar/access_right/c_abf2
dc.format.extent.none.fl_str_mv 55 pp
dc.format.mimetype.none.fl_str_mv application/pdf
dc.publisher.none.fl_str_mv Universidad del Rosario
dc.publisher.department.none.fl_str_mv Escuela de Medicina y Ciencias de la Salud
dc.publisher.program.none.fl_str_mv Especialización en Radiología
publisher.none.fl_str_mv Universidad del Rosario
institution Universidad del Rosario
dc.source.bibliographicCitation.none.fl_str_mv Foundation CF. Patient Registry 2012. Bethesda, MD Cyst Fibros Found [Internet]. 2012 Dec; Available from: http://www.tandfonline.com/doi/abs/10.1080/14608940701737359
Mateus H AP. Tamizaje Neonatal para Fibrosis Quística en una muestra de la ciudad de Bogotá. Univ del Rosario. 2011
Riordan JR, Rommens JM, Kerem BS, Alon NOA, Rozmahel R, Grzelczak Z, et al. Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA. Science (80- ). 1989;245(4922):1066–73
Fustik S. Liver cirrhosis and portal hypertension in cystic fibrosis. Srp Arh Celok Lek [Internet]. 2013;141(11–12):764–9. Available from: http://www.doiserbia.nb.rs/Article.aspx?ID=0370-81791312764F
Debray D, Kelly D, Houwen R, Strandvik B, Colombo C. Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease. J Cyst Fibros [Internet]. 2011 Jun;10(SUPPL. 2):S29–36. Available from: http://dx.doi.org/10.1016/S1569-1993(11)60006-4
Parad RB, Comeau AM, Dorkin HL, Dovey M, Gerstle R, Martin T, et al. Sweat Testing Infants Detected by Cystic Fibrosis Newborn Screening. J Pediatr [Internet]. 2005 Sep;147(3):S69–72. Available from: https://linkinghub.elsevier.com/retrieve/pii/S0022347605007602
Nishioka GJ, Cook PR. Paranasal sinus disease in patients with cystic fibrosis. Otolaryngol Clin North Am. 1996;29(1):193–206
Gergin O, Kawai K, MacDougall RD, Robson CD, Moritz E, Cunningham M, et al. Sinus Computed Tomography Imaging in Pediatric Cystic Fibrosis. Otolaryngol Neck Surg [Internet]. 2016 Jul;155(1):160–5. Available from: http://journals.sagepub.com/doi/10.1177/0194599816634671
Rybacka A, Karmelita-Katulska K. The role of computed tomography in monitoring patients with cystic fibrosis. Polish J Radiol. 2016;81:141–5
De Boeck K, Weren M, Proesmans M, Kerem E. Pancreatitis Among Patients With Cystic Fibrosis: Correlation With Pancreatic Status and Genotype. Pediatrics [Internet]. 2005 Apr 1;115(4):e463–9. Available from: http://pediatrics.aappublications.org/cgi/doi/10.1542/peds.2004-1764
Parisi GF, Di Dio G, Franzonello C, Gennaro A, Rotolo N, Lionetti E, et al. Liver Disease in Cystic Fibrosis: an Update. Hepat Mon [Internet]. 2013 Aug 14;13(8):8. Available from: http://hepatmon.com/en/articles/55392.html
Agrons GA, Corse WR, Markowitz RI, Suarez ES, Perry DR. Gastrointestinal manifestations of cystic fibrosis: radiologic-pathologic correlation. RadioGraphics [Internet]. 1996 Jul;16(4):871–93. Available from: http://pubs.rsna.org/doi/10.1148/radiographics.16.4.8835977
Lisa P, Mcevoy SH, Gibney RG, Mcmahon CJ, Heffernan EJ. Cystic Fibrosis below the Dia phragm : Abdominal Findings in Adult Patients 1. 1989;(3):1–16
Shulman LP, Elias S. Cystic fibrosis. Clin Perinatol [Internet]. 2001 Jun;28(2):383–93. Available from: https://linkinghub.elsevier.com/retrieve/pii/S0095510805700907
Chin M, Aaron SD, Bell SC. The treatment of the pulmonary and extrapulmonary manifestations of cystic fibrosis. Press Medicale [Internet]. 2017;46(6P2):e139–64. Available from: http://dx.doi.org/10.1016/j.lpm.2016.11.030
Lugo-Olivieri CH, Soyer PA, Fishman EK. Cystic fibrosis: Spectrum of thoracic and abdominal ct findings in the adult patient. Clin Imaging [Internet]. 1998 Sep;22(5):346–54. Available from: https://linkinghub.elsevier.com/retrieve/pii/S089970719800031X
Sathe MN, Freeman AJ. Gastrointestinal, Pancreatic, and Hepatobiliary Manifestations of Cystic Fibrosis. Pediatr Clin North Am [Internet]. 2016 Aug;63(4):679–98. Available from: http://dx.doi.org/10.1016/j.pcl.2016.04.008
Alexander BM, Petren EK, Rizvi S, Fink A, Ostrenga J, Sewall A. Cystic Fibrosis Patient Registry Annual Data Report 2014. Cyst Fibros Found Patient Regist [Internet]. 2014; Available from: https://www.cff.org/2014-annual-data-report
Vásquez C, Aristizábal R, Daza W. Fibrosis quística en Colombia. Registro Colombiano de Fibrosis Quistica. Primer informe. Rev Neumol Pediatr [Internet]. 2010;5(1):44–50. Available from: http://www.neumologia-pediatrica.cl
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Dodge JA. Gastrointestinal tract and nutrition in cystic fibrosis: pathophysiology. J R Soc Med. 1986;79(12):27–31.
Olveira Fuster G, Olveira C. Nutrición, fibrosis quística y aparato digestivo. Nutr Hosp. 2008;23(SUPPL. 2):71–86.
Farrell PM, White TB, Ren CL, Hempstead SE, Accurso F, Derichs N, et al. Diagnosis of Cystic Fibrosis: Consensus Guidelines from the Cystic Fibrosis Foundation. J Pediatr [Internet]. 2017;181:S4-S15.e1. Available from: http://dx.doi.org/10.1016/j.jpeds.2016.09.064
Mishra A, Greaves R, Massie J. The relevance of sweat testing for the diagnosis of cystic fibrosis in the genomic era. Clin Biochem Rev [Internet]. 2005;26(4):135–53. Available from: http://www.ncbi.nlm.nih.gov/pubmed/16648884%0Ahttp://www.pubmedcentral.nih. gov/articlerender.fcgi?artid=PMC1320177
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Aziz ZA, Davies JC, Alton EW, Wells AU, Geddes DM, Hansell DM. Computed tomography and cystic fibrosis: promises and problems. Thorax [Internet]. 2007 Feb 1;62(2):181–6. Available from: http://thorax.bmj.com/cgi/doi/10.1136/thx.2005.054379
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King LJ, Scurr ED, Murugan N, Williams SGJ, Westaby D, Healy JC. Hepatobiliary and Pancreatic Manifestations of Cystic Fibrosis: MR Imaging Appearances. RadioGraphics [Internet]. 2000 May;20(3):767–77. Available from: http://pubs.rsna.org/doi/10.1148/radiographics.20.3.g00ma08767
Soyer P, Spelle L, Pelage J-P, Dufresne A-C, Rondeau Y, Gouhiri M, et al. Cystic Fibrosis in Adolescents and Adults: Fatty Replacement of the Pancreas—CT Evaluation and Functional Correlation. Radiology [Internet]. 1999 Mar;210(3):611–5. Available from: http://pubs.rsna.org/doi/10.1148/radiology.210.3.r99mr08611
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spelling Pérez Alvarado, María Carolina3ddfaf5a-8806-40aa-95dc-21f02c4ed56a-1Pedraza Flechas, Ana María52965050Aldana Mancera, Sergio AndresSuárez Niño, Diana CarolinaEspecialista en RadiologíaMaestríaFull timed9a4337d-2b0e-49b1-9ff5-b07393922d18-1f9ab2147-f96e-4443-8fd6-f4fe6a839a36-12023-08-25T20:59:03Z2023-08-25T20:59:03Z2023-06-20En este trabajo se describen los hallazgos extrapulmonares detectados por imágenes diagnósticas, de una población colombiana con fibrosis quística, atendida en dos centros de salud de Bogotá, Colombia.This paper describes the extrapulmonary findings detected by diagnostic images of a colombian population with cystic fibrosis, treated at two health centers in Bogotá, Colombia.55 ppapplication/pdfhttps://doi.org/10.48713/10336_40772 https://repository.urosario.edu.co/handle/10336/40772spaUniversidad del RosarioEscuela de Medicina y Ciencias de la SaludEspecialización en RadiologíaAttribution-NonCommercial-NoDerivatives 4.0 InternationalAbierto (Texto Completo)EL AUTOR, manifiesta que la obra objeto de la presente autorización es original y la realizó sin violar o usurpar derechos de autor de terceros, por lo tanto la obra es de exclusiva autoría y tiene la titularidad sobre la misma. PARGRAFO: En caso de presentarse cualquier reclamación o acción por parte de un tercero en cuanto a los derechos de autor sobre la obra en cuestión, EL AUTOR, asumirá toda la responsabilidad, y saldrá en defensa de los derechos aquí autorizados; para todos los efectos la universidad actúa como un tercero de buena fe. EL AUTOR, autoriza a LA UNIVERSIDAD DEL ROSARIO, para que en los términos establecidos en la Ley 23 de 1982, Ley 44 de 1993, Decisión andina 351 de 1993, Decreto 460 de 1995 y demás normas generales sobre la materia, utilice y use la obra objeto de la presente autorización. -------------------------------------- POLITICA DE TRATAMIENTO DE DATOS PERSONALES. Declaro que autorizo previa y de forma informada el tratamiento de mis datos personales por parte de LA UNIVERSIDAD DEL ROSARIO para fines académicos y en aplicación de convenios con terceros o servicios conexos con actividades propias de la academia, con estricto cumplimiento de los principios de ley. Para el correcto ejercicio de mi derecho de habeas data cuento con la cuenta de correo habeasdata@urosario.edu.co, donde previa identificación podré solicitar la consulta, corrección y supresión de mis datos.http://creativecommons.org/licenses/by-nc-nd/4.0/http://purl.org/coar/access_right/c_abf2Foundation CF. Patient Registry 2012. Bethesda, MD Cyst Fibros Found [Internet]. 2012 Dec; Available from: http://www.tandfonline.com/doi/abs/10.1080/14608940701737359Mateus H AP. Tamizaje Neonatal para Fibrosis Quística en una muestra de la ciudad de Bogotá. Univ del Rosario. 2011Riordan JR, Rommens JM, Kerem BS, Alon NOA, Rozmahel R, Grzelczak Z, et al. Identification of the cystic fibrosis gene: Cloning and characterization of complementary DNA. Science (80- ). 1989;245(4922):1066–73Fustik S. Liver cirrhosis and portal hypertension in cystic fibrosis. Srp Arh Celok Lek [Internet]. 2013;141(11–12):764–9. Available from: http://www.doiserbia.nb.rs/Article.aspx?ID=0370-81791312764FDebray D, Kelly D, Houwen R, Strandvik B, Colombo C. Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease. J Cyst Fibros [Internet]. 2011 Jun;10(SUPPL. 2):S29–36. Available from: http://dx.doi.org/10.1016/S1569-1993(11)60006-4Parad RB, Comeau AM, Dorkin HL, Dovey M, Gerstle R, Martin T, et al. Sweat Testing Infants Detected by Cystic Fibrosis Newborn Screening. J Pediatr [Internet]. 2005 Sep;147(3):S69–72. Available from: https://linkinghub.elsevier.com/retrieve/pii/S0022347605007602Nishioka GJ, Cook PR. Paranasal sinus disease in patients with cystic fibrosis. Otolaryngol Clin North Am. 1996;29(1):193–206Gergin O, Kawai K, MacDougall RD, Robson CD, Moritz E, Cunningham M, et al. Sinus Computed Tomography Imaging in Pediatric Cystic Fibrosis. Otolaryngol Neck Surg [Internet]. 2016 Jul;155(1):160–5. Available from: http://journals.sagepub.com/doi/10.1177/0194599816634671Rybacka A, Karmelita-Katulska K. The role of computed tomography in monitoring patients with cystic fibrosis. Polish J Radiol. 2016;81:141–5De Boeck K, Weren M, Proesmans M, Kerem E. Pancreatitis Among Patients With Cystic Fibrosis: Correlation With Pancreatic Status and Genotype. Pediatrics [Internet]. 2005 Apr 1;115(4):e463–9. Available from: http://pediatrics.aappublications.org/cgi/doi/10.1542/peds.2004-1764Parisi GF, Di Dio G, Franzonello C, Gennaro A, Rotolo N, Lionetti E, et al. Liver Disease in Cystic Fibrosis: an Update. Hepat Mon [Internet]. 2013 Aug 14;13(8):8. Available from: http://hepatmon.com/en/articles/55392.htmlAgrons GA, Corse WR, Markowitz RI, Suarez ES, Perry DR. Gastrointestinal manifestations of cystic fibrosis: radiologic-pathologic correlation. RadioGraphics [Internet]. 1996 Jul;16(4):871–93. Available from: http://pubs.rsna.org/doi/10.1148/radiographics.16.4.8835977Lisa P, Mcevoy SH, Gibney RG, Mcmahon CJ, Heffernan EJ. Cystic Fibrosis below the Dia phragm : Abdominal Findings in Adult Patients 1. 1989;(3):1–16Shulman LP, Elias S. Cystic fibrosis. Clin Perinatol [Internet]. 2001 Jun;28(2):383–93. Available from: https://linkinghub.elsevier.com/retrieve/pii/S0095510805700907Chin M, Aaron SD, Bell SC. The treatment of the pulmonary and extrapulmonary manifestations of cystic fibrosis. Press Medicale [Internet]. 2017;46(6P2):e139–64. Available from: http://dx.doi.org/10.1016/j.lpm.2016.11.030Lugo-Olivieri CH, Soyer PA, Fishman EK. Cystic fibrosis: Spectrum of thoracic and abdominal ct findings in the adult patient. Clin Imaging [Internet]. 1998 Sep;22(5):346–54. Available from: https://linkinghub.elsevier.com/retrieve/pii/S089970719800031XSathe MN, Freeman AJ. Gastrointestinal, Pancreatic, and Hepatobiliary Manifestations of Cystic Fibrosis. 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